Desmoplastic Infantile Astrocytoma in a 47-day Old Male Infant with Four-year Follow-up: A Rare Case Report and Literature Review


Desmoplastic infantile astrocytoma/ganglioglioma (DIA/DIG) is a rare mixed neuronalglial solid cystic brain tumor found in infantile cerebral hemispheres. The main presentation of the tumor is the rapidly enlarging of the head circumference with hydrocephalus and seizure. DIA is classified as a WHO Grade 1 brain tumor but, due to the rarity of the tumor, few studies are available on tumor survival and prognosis. Herein, we report a 47-day-old male infant diagnosed with DIA and the four-year follow-up.


brain neoplasm, astrocytoma, pediatric neurosurgery, oncology, desmoplastic cerebral astrocytoma of infancy, desmoplastic infantile ganglioglioma

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