Glaucoma in Ectropion Uveae Syndrome: a Case Report and Literature Review


Purpose: To report a case of advanced childhood glaucoma secondary to congenital ectropion uveae (CEU).

Case Report: The patient was a seven-year-old boy with unilateral glaucoma secondary to CEU and facial asymmetry, mild unilateral ptosis, and proptosis in the left eye. The intraocular pressure (IOP) was 28 mmHg and cup-to-disc ratio was 0.8 in the left eye. After starting glaucoma medication, IOP decreased to 21 mmHg. In view of the uncontrolled IOP with medication and high cup-to-disc ratio and increased axial length of the left eye, mitomycin-C (MMC)-augmented trabeculectomy was planned. Despite sub-tenon MMC injection and bleb needling, the bleb failed after six months, and we had to perform a shunt procedure to control the IOP.

Conclusion: Although CEU is rare, ophthalmologists should be familiar with this syndrome because of the high frequency of glaucoma and its challenging management during childhood.


Congenital Ectropion Uveae; Facial Hemihypertrophy; Intraocular Pressure; Mitomycin-C; Ptosis; Secondary Glaucoma

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