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Hatami M, Doozandeh A, Feizi M. Glaucoma in Ectropion Uveae Syndrome: a Case Report and Literature Review. JOVR [Internet]. 2019Jul.18 [cited 2024Apr.26];14(3):370–375. Available from: https://knepublishing.com/index.php/JOVR/article/view/4793

https://doi.org/10.18502/jovr.v14i3.4793

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authors

  • Mohammadmehdi Hatami

    Mohammadmehdi Hatami

    Ophthalmic Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran
    https://orcid.org/0000-0003-2733-7802
  • Azadeh Doozandeh

    Azadeh Doozandeh

    Ophthalmic Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran
  • Mohadeseh Feizi

    Mohadeseh Feizi

    Ophthalmic Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran

Published Date

  • Jul 18, 2019
This journal is publishing all the articles under Creative Commons Attribution License CC BY 4.0.

Glaucoma in Ectropion Uveae Syndrome: a Case Report and Literature Review

Journal of Ophthalmic and Vision Research (JOVR) / July–September 2019, Volume 14, Issue 3 / Pages 370–375

Abstract

Purpose: To report a case of advanced childhood glaucoma secondary to congenital ectropion uveae (CEU).


Case Report: The patient was a seven-year-old boy with unilateral glaucoma secondary to CEU and facial asymmetry, mild unilateral ptosis, and proptosis in the left eye. The intraocular pressure (IOP) was 28 mmHg and cup-to-disc ratio was 0.8 in the left eye. After starting glaucoma medication, IOP decreased to 21 mmHg. In view of the uncontrolled IOP with medication and high cup-to-disc ratio and increased axial length of the left eye, mitomycin-C (MMC)-augmented trabeculectomy was planned. Despite sub-tenon MMC injection and bleb needling, the bleb failed after six months, and we had to perform a shunt procedure to control the IOP.


Conclusion: Although CEU is rare, ophthalmologists should be familiar with this syndrome because of the high frequency of glaucoma and its challenging management during childhood.

Keywords:

Congenital Ectropion Uveae; Facial Hemihypertrophy; Intraocular Pressure; Mitomycin-C; Ptosis; Secondary Glaucoma

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