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Behboudi H, Zayeni H, Haji-Abbasi A, Azaripour E, Alizadeh Y, Soltani-Moghadam R. Coats’-like Response Associated with Linear Scleroderma. JOVR [Internet]. 2022Jan.21 [cited 2024Apr.24];17(1):135–139. Available from: https://knepublishing.com/index.php/JOVR/article/view/10179

https://doi.org/10.18502/jovr.v17i1.10179

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authors

  • Hassan Behboudi

    Hassan Behboudi

    Eye Research Center, Department of Eye, Amiralmomenin Hospital, School of Medicine, Guilan University of Medical Sciences, Rasht, Iran
  • Habib Zayeni

    Habib Zayeni

    Rheumatology Research Center, Razi Hospital, School of Medicine, Guilan University of Medical Sciences, Rasht, Iran
  • Asghar Haji-Abbasi

    Asghar Haji-Abbasi

    Rheumatology Research Center, Razi Hospital, School of Medicine, Guilan University of Medical Sciences, Rasht, Iran
  • Ebrahim Azaripour

    Ebrahim Azaripour

    Eye Research Center, Department of Eye, Amiralmomenin Hospital, School of Medicine, Guilan University of Medical Sciences, Rasht, Iran
  • Yousef Alizadeh

    Yousef Alizadeh

    Eye Research Center, Department of Eye, Amiralmomenin Hospital, School of Medicine, Guilan University of Medical Sciences, Rasht, Iran
  • Reza Soltani-Moghadam

    Reza Soltani-Moghadam

    Eye Research Center, Department of Eye, Amiralmomenin Hospital, School of Medicine, Guilan University of Medical Sciences, Rasht, Iran

Published Date

  • Jan 21, 2022
This journal is publishing all the articles under Creative Commons Attribution License CC BY 4.0.

Coats’-like Response Associated with Linear Scleroderma

Journal of Ophthalmic and Vision Research (JOVR) / January–March 2022, Volume 17, Issue 1 / Pages 135–139

Abstract

Purpose: To present a case of linear scleroderma known as “en coup de sabre” associated with Coats’- like response.


Case Report: A 12-year-old boy presented with subacute painless vision loss in the ipsilateral side of the patient’s en coup de sabre lesion. Ocular examination revealed vitreous hemorrhage with severe exudation of the posterior pole and telangiectatic vessels. Fundus fluorescein angiography indicated multiple vascular beadings and fusiform aneurysms with leakage which was consistent with a Coats’-like response. The patient was subsequently treated with intravitreal bevacizumab and targeted retinal photocoagulation. Twelve months’ follow-up showed marked resolution of macular exudation with significant visual improvement.


Conclusion: Physicians should be aware of the possible ophthalmic disorders accompanying en coup de sabre and careful ophthalmologic examinations should be performed in these patients. As presented in the current case, treatment with intravitreal anti-VEGF agents and laser photocoagulation may be a beneficial option for patients with coats’-like response.

Keywords:

Bevcizumab, Coat’s Disease, Craniofacial, En Coup de Sabre, Scleroderma

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